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Titre	Best-Corrected Visual Acuity and Foveal Location in Patients with Congenital Stationary Night Blindness
Abstract Nr.	1058

But	To evaluate best-corrected visual acuity and foveal location in patients with congenital stationary night blindness (CSNB) with Schubert-Bornschein type electroretinographies (ERG), of the Miyake Complete (cCSNB) and Incomplete (iCSNB) types.
Méthodes	In this mixed retro- and prospective study, data on 22 cCSNB and 14 Miyake iCSNB patients were obtained. All available ophthalmological clinical findings, in addition to Goldmann visual field tests, full-field and ON-OFF ERGs, white, infrared and blue light fundus pictures, OCT images and genetic testing results were studied.
Résultats	Data on 72 eyes of 35 X-linked patients (21 cCSNB & 14 iCSNB) and 1 AR cCSNB patient were included in the study. Mean decimal best-corrected visual acuities were 0,43 ± 0,23 for RE and 0,37 ± 0,24 for LE, mean refractive values were -7,28 ± 4,42D for RE and -7,31 ± 5,06D for the LE. Nineteen patients had nystagmus, 14 patients had either strabismus or had undergone strabismus surgery. Foveal ectopia was observed in 30 eyes (14 cCNSB and 8 iCSNB). Macular staphylomata were seen in 14 eyes, foveal hypoplasia was noted in 4 eyes.
Conclusion	Best-corrected visual acuity is significantly lower in CSNB patients. Nearly half of the patients had either foveal ectopia or maldevelopment.

Auteur 1

Nom	KARABULUT
Initiales	E
Institut	Dept of Ophthalmology Ghent University Hospital; Ophthalmology Clinic,Elmadag State Hospital
Ville	Ghent, Belgium; Ankara, Turkey

Auteur 2

Nom	WALRAEDT
Initiales	S
Institut	Dept of Ophthalmology Ghent University Hospital
Ville	Ghent, Belgium

Auteur 3

Nom	DE ZAEYTIJD
Initiales	J
Institut	Dept of Ophthalmology Ghent University Hospital
Ville	Ghent, Belgium

Auteur 4

Nom	DELBEKE
Initiales	P
Institut	Dept of Ophthalmology Ghent University Hospital
Ville	Ghent, Belgium

Auteur 5

Nom	LEROY
Initiales	B.P
Institut	Dept of Ophthalmology & Ctr for Medical Genetics, Ghent University Hospital;Div of Ophthalmology &
Ville	Ghent, Belgium;